Abstract
Background: Congenitally absent cystic duct is a rare anomaly with significant surgical implications. Only 11 clear cases of congenitally absent cystic ducts have been reported.
Case presentation: A 16-year-old male was admitted in February 2013 complaining of recurrent right upper abdominal pain, vomiting, and fatty dyspepsia. The gallbladder was hugely distended, severely inflamed, congenital abnormalities found out; no cystic duct was found. Choleduchojejunostomy was performed. The 1-week post-operative patient was referred to a specialized center by the hepatobiliary surgeon, magnetic
resonance cholangiopancreatography was performed, it was normal, no leak, patient stayed for few days (10 days) then discharged from there.
Conclusion: The absent cystic duct is rare and only 11 cases have been reported and the first case was described in 1921. Agenesis is discovered incidentally and awareness of the possibility of this anomaly decreases the risk of complication. In this report, we described a case of a congenitally absent cystic duct and provide a comprehensive discussion of the clinical significance and appropriate surgical management of this anomaly.

Key words: Cystic duct, congenital absence, absent cystic duct